Congenital lymphangiomatosis: Multidisciplinary approach
In: Journal of Pediatric Surgery Case Reports, Jg. 61 (2020-10-01), Heft 101621-
Online
academicJournal
Zugriff:
Background: Diffuse lymphangiomatosis is a rare disorder of the lymphatic vessels. Its prognosis is poor and its treatment not codified. Methods: We describe the case of a 14 years old boy known for a lymphatic malformation of the left chest wall with pleuropulmonary, bone and visceral involvement. He presented with respiratory difficulties and a left pleural effusion. The treatment associated thoracic drainage, surgical pleurectomy and iterative sclerotherapy. Results: The patient is currently asymptomatic. On imaging, there is a decrease of the left lateral thoracic component and a resolution of the intra-pleural portion. Conclusions: The treatment of diffuse lymphangiomatosis is based on a multimodal management.
Titel: |
Congenital lymphangiomatosis: Multidisciplinary approach
|
---|---|
Autor/in / Beteiligte Person: | Oumama El Ezzi ; Saliou, Guillaume ; Gengler, Carole ; Anthony de Buys Roessingh |
Link: | |
Zeitschrift: | Journal of Pediatric Surgery Case Reports, Jg. 61 (2020-10-01), Heft 101621- |
Veröffentlichung: | Elsevier, 2020 |
Medientyp: | academicJournal |
ISSN: | 2213-5766 (print) ; 4746-2493 (print) |
DOI: | 10.1016/j.epsc.2020.101621 |
Schlagwort: |
|
Sonstiges: |
|